Adult-type aortic coarctation associated with type 0 bicuspid aortic valve and single coronary artery: case report
DOI:
https://doi.org/10.37615/retic.v9n2a13Keywords:
congenital heart diseases, aortic coarctation, aortic valve, coronary vessel anomalies, case reportsAbstract
Aortic coarctation is a congenital heart disease that may remain undiagnosed until adulthood, particularly when the obstruction is moderate or associated with other anatomical variants. It is frequently associated with bicuspid aortic valve and, less commonly, with congenital coronary anomalies. Recognition of these associations is important because of their diagnostic and surgical implications in adult patients with aortic pathology. We report the case of a 63-year-old man with post-stenotic dilatation of the descending thoracic aorta secondary to adult-type aortic coarctation. During his evaluation, a bicuspid aortic valve without raphe (Sievers type 0) and a single left
coronary artery origin with a single coronary ostium were incidentally identified. The patient underwent coronary computed tomography angiography, which allowed precise characterization of the aortic, valvular, and coronary anatomy. Results: Imaging confirmed the presence of aortic coarctation with post-stenotic dilatation, type
0 bicuspid aortic valve, and a single origin of the left coronary artery, findings relevant for therapeutic planning. This case highlights the importance of considering undiagnosed adult congenital heart disease in patients with aortic pathology. Comprehensive anatomical evaluation using computed tomography angiography is essential
for accurate diagnosis and appropriate management planning.
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Copyright (c) 2026 Miguel Ayala-Leon, Daniela Andrea Macias-Hernández, Adriana Manriquez-Hernandez, Julia Pereira-Forcado, Arturo Evangelista
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