Marfan Syndrome and mitral annulus disjunction
DOI:
https://doi.org/10.37615/retic.v7n1a9Keywords:
mitral annulus disjunction, Marfan syndrome, sudden cardiac deathAbstract
We present a case of Marfan syndrome with severe aortic insufficiency in which mitral annulus disjunction is demonstrated. Mitral annulus disjunction (MAD) is characterized by a displacement between the junction of the annulus with the ventricular myocardium. The significance of this abnormality is its association with ventricular arrhythmias and sudden cardiac death. There is a relationship between the size of the disjunction with the risk of ventricular tachycardia; it has been identified that the greater the displacement, the greater the risk of sudden cardiac death.
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Copyright (c) 2024 Arnold Hernández, Denisse Guzmán Ramírez
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