Middle aortic syndrome in adulthood. A clinical case report

Authors

  • Isabel Molina Borao Paediatric Cardiology and Congenital Heart Disease Service. Hospital Universitario Ramón y Cajal. Madrid. Spain
  • María Álvarez Fuente Paediatric Cardiology and Congenital Heart Disease Service. Hospital Universitario Ramón y Cajal. Madrid. Spain
  • Tomasa Centella Hernández Children's Cardiac Surgery and Congenital Heart Disease Service. Hospital Universitario Ramón y Cajal. Madrid. Spain
  • Jesús Javier Martín Pinacho Radiology department. Hospital Universitario Ramón y Cajal. Madrid. Spain
  • Inmaculada Sánchez Pérez Paediatric Cardiology and Congenital Heart Disease Service. Hospital Universitario Ramón y Cajal. Madrid. Spain
  • Natalia Rivero Jiménez Paediatric Cardiology and Congenital Heart Disease Service. Hospital Universitario Ramón y Cajal. Madrid. Spain
  • Maria Jesus del Cerro Marín Paediatric Cardiology and Congenital Heart Disease Service. Hospital Universitario Ramón y Cajal. Madrid. Spain

DOI:

https://doi.org/10.37615/retic.v6n1a4

Keywords:

middle aortic syndrome, coarctation of the descending and abdominal aorta, aortic CT scan, extraanatomic aorto-aortic bypass

Abstract

We present the case of a 35-year-old patient with a diagnosis of congenital middle aortic syndrome corrected in childhood with aortic bypass interposition of a Dacron conduit. During follow-up, she was diagnosed with arterial hypertension, for which antihypertensive treatment was started and a stent was implanted in the conduit. A control CT of the aorta revealed a rib lesion suggestive of osteochondroma that compressed the duct. Cardiac catheterization confirmed hemodynamic stenosis due to extrinsic compression of the rib lesion at the level of the previously implanted stent. The CT imaging study helped to diagnose a complication at the level of the aorta that was  undetected in other imaging techniques.

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Published

2023-04-30

How to Cite

1.
Molina Borao I, Álvarez Fuente M, Centella Hernández T, Martín Pinacho JJ, Sánchez Pérez I, Rivero Jiménez N, del Cerro Marín MJ. Middle aortic syndrome in adulthood. A clinical case report. Rev Ecocardiogr Pract Otras Tec Imag Card (RETIC) [Internet]. 2023 Apr. 30 [cited 2024 Jul. 27];6(1):22-5. Available from: https://imagenretic.org/RevEcocarPract/article/view/575