Restrictive cardiomyopathy due to light chain amyloidosis. Post CYBORD improvement.

Authors

  • Zuilma Yurith Vasquez Ortiz National Institute of Medical Science and Nutrition Salvador Zuviran
  • Adriana E. Viñas Mendieta Marine Medical Center "Cirujano Santiago Tavara"
  • Rolando D. Ramirez Cervantes National Institute of Medical Sciences and Nutrition Salvador Zubiran
  • Sandra Rosales Uvera National Isntitute of Medical Sciences and Nutrition Salvador Zubiran
  • Maria Jose LIzardo National Institute of Medical Sciences and Nutrition Salvador Zubiran

DOI:

https://doi.org/10.37615/retic.v5n3a7

Keywords:

amiloidosis, echocardiography, heart failure

Abstract

AL cardiac amyloidosis is a disease caused by extracellular deposition of insoluble proteins; Without treatment, survival is usually less than six months after the onset of symptoms of heart failure. The CYBORD-D scheme is the first choice for its safety and favorable evolution. We present the case of a patient with AL amyloidosis with symptoms of severe cardiac and extracardiac dysfunction, also with all laboratory and echocardiographic parameters of poor prognosis. At one year of follow-up, after eight cycles of the CYBORD regimen, presented great clinical improvement, complete hematological response, decrease in cardiac biomarkers and favorable progress in cardiac function.

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References

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Published

2022-12-31

How to Cite

1.
Vasquez Ortiz ZY, Viñas Mendieta AE, Ramirez Cervantes RD, Rosales Uvera S, Jose LIzardo M. Restrictive cardiomyopathy due to light chain amyloidosis. Post CYBORD improvement. Rev Ecocardiogr Pract Otras Tec Imag Card (RETIC) [Internet]. 2022 Dec. 31 [cited 2024 Jul. 3];5(3):31-6. Available from: https://imagenretic.org/RevEcocarPract/article/view/493

Issue

Vol. 5 No. 3 (2022): Journal of Practical Echocardiography and Other Cardiac Imaging Techniques

Section

CLINICAL CASES

License

Copyright (c) 2022 Zuilma Yurith Vasquez Ortiz, Adriana E. Viñas Mendieta, Rolando D. Ramirez Cervantes, Sandra Rosales Uvera, Maria Jose Lizardo

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This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.

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