Double interatrial septum: an extremely rare congenital heart defect

Authors

  • Francina Frías Adult Cardiology. CEDIMAT Cardiovascular Center. Santo Domingo. Dominican Republic
  • Elvis Rivera Adult Cardiology. CEDIMAT Cardiovascular Center. Santo Domingo. Dominican Republic
  • Yenny Espinal Adult Cardiology. CEDIMAT Cardiovascular Center. Santo Domingo. Dominican Republic
  • César Herrera Adult Cardiology. CEDIMAT Cardiovascular Center. Santo Domingo. Dominican Republic

DOI:

https://doi.org/10.37615/retic.v3n1a9

Keywords:

cardiac congenital anomaly, double atrial septum, atrial chamber.

Abstract

Double atrial septum (DAS) is a very rare atrial septal anomaly in which there is a duplicated septum with a persistent interatrial cavity between these two chambers, however, embryologically, is presumably a persistent left venous valve of the sinus venosus. So far, there are only 14 reported cases in adults without other associated congenital anomalies, some of which are related to systemic embolic events. We present the case of a 44-year-old woman with DAS and interatrial cavity without communication to either atrium and without relationship with embolisms.

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References

Deegan RJ, Eagle S. Incidental Finding of a Double Interatrial Septum in a Patient Undergoing Atrial Fibrillation Ablation. Cardiovascular Imaging Case Report Journal 2018; 3 (2): 92-94. doi: https://doi.org/10.1016/j.case.2017.10.009

Li X, Zhu D, Tang H, et al. Double Atrial Septum with Interatrial Chamber Formation and Recurrent Paradoxical Embolism. Annals of Thoracic and Cardiovascular Surgery 2014; 20 (Supplement): 829-831. doi: https://doi.org/10.5761/atcs.cr.12.02176

Roberson DA, Javois AJ, Cui W, et al. Double atrial septum with persistent interatrial space: echocardiographic features of a rare atrial septal malformation. J Am Soc Echocardiogr 2006; 19: 1175-1181. doi: https://doi.org/10.1016/j.echo.2006.04.001

Harding JD, Grzywacz F, Sangrigoli R. Double atrial septum and transseptal puncture: an unusual obstacle to pulmonary vein isolation. Heart Rhythm 2011; 8: 1457-1458. doi: https://doi.org/10.1016/j.hrthm.2010.05.005

Published

2020-04-30

How to Cite

1.
Frías F, Rivera E, Espinal Y, Herrera C. Double interatrial septum: an extremely rare congenital heart defect. Rev Ecocardiogr Pract Otras Tec Imag Card (RETIC) [Internet]. 2020 Apr. 30 [cited 2024 Jul. 3];3(1):35-7. Available from: https://imagenretic.org/RevEcocarPract/article/view/216