Dehiscencia completa de tubo valvulado aórtico, evaluación y correlación entre eco doppler color y tomografía multislice cardíaca. Reporte de caso
DOI:
https://doi.org/10.37615/retic.v9n1a5Keywords:
Marfan syndrome, aortic aneurysm, heart valve prosthesis, postoperative complications, case reportsAbstract
Aortic dilation is found in approximately 50-83 % of children with Marfan syndrome and progresses over time. Prophylactic aortic root repair has had the greatest impact on the survival of patients with MFS and a dilated aortic root. In its elective form, proximal aortic replacement has 30-day morbidity and mortality of 1.5 %. However, emergency replacement (within 24 h of consultation) is associated with increased 30-day mortality by 11.7 %. This underscores the importance of carefully timing elective surgical intervention to avoid the increased risk with emergency operations.
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