Undifferentiated malignant pleomorphic sarcoma in the left atrium. Case report

Authors

  • Libardo Marmolejo Valois Cardiology. Cardioinfantil Foundation La Cardio. Bogota, Colombia.
  • Pablo Antonio Guerra Leon Atención Cardiocirculatoria. Hospital Universitario Mayor Méderi / Alianza Cardiovascular. Bogotá, Colombia.
  • Jenny Patricia Galindo Varela Cardiovascular Health Program, National University Hospital. Bogota Colombia.
  • Laura Catalina Arcos Medina Atención Cardiocirculatoria. Hospital Universitario Mayor Méderi / Alianza Cardiovascular. Bogotá, Colombia.
  • Nubia Esperanza Carrero Rojas Atención Cardiocirculatoria. Hospital Universitario Mayor Méderi / Alianza Cardiovascular. Bogotá, Colombia.

DOI:

https://doi.org/10.37615/retic.v6n3a5

Keywords:

primary cardiac tumors, sarcoma, pleomorphic

Abstract

The incidence of malignant primary cardiac tumors is very low and they present a poor prognosis due to local recurrence, with very poor survival. This type of tumors presents nonspecific symptoms and its presentation usually occurs in advanced stages of the disease. Surgical resection is the initial treatment, adyuvant chemoterapy and radiation therapy are often palliative options since the prognosis despite these therapies is one year or less. We present the case of a patient with undifferentiated malignant pleomorphic sarcoma with aggressive presentation and early recurrence despite surgical resection

Downloads

Download data is not yet available.

Metrics

Metrics Loading ...

References

Bandyopadhyay S, Banerjee S, Paul A, Das RK. Primary malignant fibrous histiocytoma involving the left pulmonary vein presenting as a left atrial tumor. Ann Card Anaesth. 2013;16(4):293-5. doi: https://doi.org/10.4103/0971-9784.119184 DOI: https://doi.org/10.4103/0971-9784.119184

Simpson L, Kumar SK, Okuno SH, Schaff HV, Porrata LF, Buckner JC, et al. Malignant primary cardiac tumors: review of a single institution experience. Cancer. 2008;112(11):2440-6. doi: https://doi.org/10.1002/cncr.23459 DOI: https://doi.org/10.1002/cncr.23459

Maraj S, Pressman GS, Figueredo VM. Primary cardiac tumors. Int J Cardiol.2009;133(2):152-6. doi: https://doi.org/10.1016/j.ijcard.2008.11.103 DOI: https://doi.org/10.1016/j.ijcard.2008.11.103

Randhawa JS, Budd GT, Randhawa M, Ahluwalia M, Jia X, Daw H, et al. Primary Cardiac Sarcoma: 25-Year Cleveland Clinic Experience. Am J Clin Oncol. 2016;39(6):593-9. doi: https://doi.org/10.1097/COC.0000000000000106 DOI: https://doi.org/10.1097/COC.0000000000000106

Brooks JS, Lee S. Contemporary diagnostics: sarcoma pathology update. J Surg Oncol. 2015;111(5):513-9. doi: https://doi.org/10.1002/jso.23853 DOI: https://doi.org/10.1002/jso.23853

Pobirci DD, Bogdan F, Pobirci O, Petcu CA, Roşca E. Study of malignant fibrous histiocytoma: clinical, statistic and histopatological interrelation. Rom J Morphol Embryol. 2011;52(1 Suppl):385-8.

Carrero N, Salazar G, Guerrero AF, Mugnier J, Medina HM. Recurrent Undifferentiated Pleomorphic Sarcoma in the Left Atrium. CASE (Phila). 2018;2(2):38-41. doi: https://doi.org/10.1016/j.case.2017.07.003 DOI: https://doi.org/10.1016/j.case.2017.07.003

Bossert T, Gummert JF, Battellini R, Richter M, Barten M, Walther T, et al. Surgical experience with 77 primary cardiac tumors. Interact Cardiovasc Thorac Surg. 2005;4(4):311-5. doi: https://doi.org/10.1510/icvts.2004.103044 DOI: https://doi.org/10.1510/icvts.2004.103044

Published

2023-12-30

How to Cite

1.
Marmolejo Valois L, Guerra Leon PA, Galindo Varela JP, Arcos Medina LC, Carrero Rojas NE. Undifferentiated malignant pleomorphic sarcoma in the left atrium. Case report. Rev Ecocardiogr Pract Otras Tec Imag Card (RETIC) [Internet]. 2023 Dec. 30 [cited 2024 Jul. 3];6(3):23-6. Available from: https://imagenretic.org/RevEcocarPract/article/view/442