Transposition of great arteries and a rare extracardiac association, that will question what is the best conduct to follow
DOI:
https://doi.org/10.37615/retic.v3n2a4Keywords:
transposition of great arteries, pulmonary agenesis, extracardiac association.Abstract
Transposition of great arteries is one of the most common and severe congenital heart diseases, but also one of the most mysterious. It represents 5% of all congenital heart diseases and 34% of trunk-cone defects with situs solitus. Without treatment, 30% of cases die before the first month and 90% before the first year. We present a case of a patient with this heart disease, in whom the common images do not meet the diagnostic criteria, because a rare extracardiac association (left pulmonary agenesis) would change the clinical management.
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Copyright (c) 2020 Karen Condori Alvino, Carlos Álvarez Murillo
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