Vascular ring due to double aortic arch in a patient with mitral stenosis, left Komerell´s diverticulum and 22q11.2 syndrome
DOI:
https://doi.org/10.37615/retic.v7n2a11Keywords:
vascular ring, double aortic arch, 22q11.2, Kommerell's diverticulumAbstract
Vascular rings are a diagnostic challenge for clinicians requiring a multidisciplinary approach and diagnostic augmentation by imaging techniques like computed tomography in patients suspected of having this pathology. The primary clinical characteristics of vascular rings are respiratory and/or gastrointestinal problems. The origin of the supra-aortic vessels and the vascular structures that form them are used to categorize vascular rings, all of which are influenced by embryological defects of the primitive aortic arches. Kommerell's diverticulum is a remnant of the aortic arch that gives rise to an aneurysmal dilation from which one of the supra-aortic vessels originates. We present the case of an 11-year-old patient with a previous cardiac surgery who presented with dysphagia and dyspnea. The echocardiogram revealed a right aortic arch, leading to the decision to request an angiotomography, which resulted in the diagnosis of vascular ring with a double arch with right dominance and left atresia, left Kommerell's diverticulum, and persistent ductus arteriosus.
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Copyright (c) 2024 Óscar Andrés Ramírez Terán, Maximiliano Rodríguez , Eduardo Tomás Alvarado
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