Persistent left superior vena cava associated with atrial septal defect type sinus venosus superior vena cava and anomalous partial drainage of pulmonary veins

Authors

  • José Antonio Ortiz de Murua Servicio de Cardiología. Complejo Hospitalario Universitario de Santiago de Compostela. Santiago de Compostela. España
  • José Ignacio Martín-Leal Servicio de Cardiología. Complejo Hospitalario Universitario de Santiago de Compostela. Santiago de Compostela. España
  • María Ruiz-Olgado Servicio de Cardiología. Complejo Hospitalario Universitario de Santiago de Compostela. Santiago de Compostela. España
  • Irene Blanco-Martínez Servicio de Cardiología. Complejo Hospitalario Universitario de Santiago de Compostela. Santiago de Compostela. España
  • José Luis Santos-Iglesias Servicio de Cardiología. Complejo Hospitalario Universitario de Santiago de Compostela. Santiago de Compostela. España

DOI:

https://doi.org/10.37615/retic.v1n2a13

Keywords:

persistent left superior vena cava, superior sinus venous atrial septal defect, unroofed coronary sinus.

Abstract

We present an unusual clinical case of a patient with a superior sinus venous atrial septal defect, partial anomalous pulmonary venous drainage and persistent left superior vena cava (PLSVC). The latter entity is a relatively frequent finding in patients with congenital heart disease (6.1%) and, therefore, can be observed in patients with superior sinus venous interatrial communication. However, PLSVC is clearly associated with coronary sinus type defects (a very infrequent entity). We will use this clinical case to show how to asses both defects by echocardiography, emphasizing the diagnostic value of the available cardiac imaging techniques.

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References

Talwae S, Upadhyay M, Choudhary SK, et al. Interatrial communication with unusual caval venous anomalies. World J Pediatric Congenit Heart Surg 2010; 1 (3): 400-403. DOI: https://doi.org/10.1177/2150135110379621

Tretter JT, Chikkabyrappa S, Spicer DE, et al. Understanding the spectrum of sinus venosus interatrial communications. Cardiol Young 2017; 27 (3): 418-426. DOI: https://doi.org/10.1017/S1047951116000664

Al Zaghal AM, Li J, Anderson RH, et al. Anatomical criteria of the diagnosis of sinus venosus defects. Heart 1997; 78 (3): 298-304. DOI: https://doi.org/10.1136/hrt.78.3.298

Kula S, Cevik A, Sanli C, et al. Persistent left superior vena cava: experience of a tertiary health-care center. Pediatric Int 2011; 53 (6): 1066-1069. DOI: https://doi.org/10.1111/j.1442-200X.2011.03443.x

Ratliff HL, Yousufuddin M, Lieving WR, et al. Persistent left superior vena cava: case reports and clinical implications. Int J Cardiol 2006; 113: 242-246. DOI: https://doi.org/10.1016/j.ijcard.2005.08.067

Troost E, Gewillig M, Budts W. Percutaneous closure of a persistent left superior vena cava connected to the left atrium. Int J Cardiol 2006; 106: 365-366. DOI: https://doi.org/10.1016/j.ijcard.2005.02.015

Sarodia BD, Stoller JK. Persistent left superior vena cava: case report and literature review. Respir Care 2000; 45: 411-426.

Zhi AH, Dai RP, Ma WG, et al. CT angiography for diagnosis and subcategorization of unroofed coronary sinus syndrome. J Thorac Dis 2017; 9 (10): 3946-3955. DOI: https://doi.org/10.21037/jtd.2017.09.03

Published

2018-08-31

How to Cite

1.
Ortiz de Murua JA, Martín-Leal JI, Ruiz-Olgado M, Blanco-Martínez I, Santos-Iglesias JL. Persistent left superior vena cava associated with atrial septal defect type sinus venosus superior vena cava and anomalous partial drainage of pulmonary veins. Rev Ecocardiogr Pract Otras Tec Imag Card (RETIC) [Internet]. 2018 Aug. 31 [cited 2024 Jul. 3];1(2):55-7. Available from: https://imagenretic.org/RevEcocarPract/article/view/186

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