Hypertrophic cardiomyopathy associated with Cor Triatriatum. The importance of multimodality in cardiac imaging.
DOI:
https://doi.org/10.37615/retic.v5n2a12Keywords:
hypertrophic cardiomyopathy, Cor Triatriatum, Global Longitudinal Strain, late gadolinium enhancement.Abstract
We present the case of a 19-year-old patient who, after detecting a heart murmur on physical examination, was diagnosed with hypertrophic cardiomyopathy on echocardiography. He maintains preserved left ventricular systolic function, but very low Global Longitudinal Strain values. Cardiac magnetic resonance imaging shows the presence of extensive late gadolinium enhancement and also identifies a Cor Triatriatum that had gone unnoticed by echocardiography. A high risk of sudden death was calculated and it was decided to implant an automatic defibrillator.
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Ather B, Meredith A, Siddiqui WJ. Cor Triatriatum. 2021 Sep 28. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2022 Jan–. PMID: 30480976.
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Copyright (c) 2022 Pablo Esteban Auquilla Clavijo, Marina Povar Echeverría, Berta Daga Calejero, Verónica Aliaga Rivas-O´neill, Marta Aliacar Muñoz
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