Endocardial fibroelastosis as a rare cause of cardiomyopathy
DOI:
https://doi.org/10.37615/retic.n1a12Keywords:
Endocardial fibroelastosis, Heart transplantation, Restrictive cardiomyopathy.Abstract
A 42-year-old male with coarctation of the aorta treated with surgery as a teenager presented with progressive heart failure, eventually requiring cardiac transplantation. The diagnosis of the imaging tests, confirmed by pathology, was restrictive cardiomyopathy due to endocardial fibroelastosis with extensive calcification. The main imaging findings in this patient are presented, and the most relevant clinical features of this rare disease are discussed.
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Copyright (c) 2016 Elena Rodríguez González, Miguel Ángel Cavero, Vanessa Moñivas, Jesús Mirelis, Javier Segovia
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