When the simple communication interatrial is not so simple
DOI:
https://doi.org/10.37615/retic.n1a10Keywords:
Atrial septal defect, Pulmonary hypertension, Eisenmenger, Thrombosis.Abstract
Pulmonary hypertension (PAH) aff ects 5 to 10% of patients with congenital heart disease. The long-term survival is variable, observing heterogeneous behavior related to defect location, size, pulmonary vascular resistance, or progression of PAH after surgical correction. We submit the case about a young woman, carrying an atrial septal of intermediate size, with shortcut inversion, severe arterial desaturation, aneurysmal pulmonary artery, and extensive thrombosis of its branches, a condition that has induced pulmonary vascular hyperresistance and the Eisenmenger physiology.
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Copyright (c) 2022 María Elena Sánchez, Marcelo Simón Cohen, Victor Daniel Darú, Jorge Lowenstein
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