Primary cardiac angiosarcoma

Authors

  • Melissa Rodríguez Israel Laboratorio de Ecocardiografía, Servicio de Cardiología. Hospital San Vicente Paúl. San José, Costa Rica
  • Eduardo Alvarado Sánchez Laboratorio de Ecocardiografía, Servicio de Cardiología. Hospital San Vicente Paúl. San José, Costa Rica
  • José Mena Sandí Departamento de Anatomía Patológica. Hospital México. San José, Costa Rica
  • Eva Moreno Medina Departamento de Anatomía Patológica. Hospital México. San José, Costa Rica

DOI:

https://doi.org/10.37615/retic.v1n2a8

Keywords:

cardiac tumor, primary angiosarcoma, pulmonary hypertension, Tako-Tsubo.

Abstract

Cardiac primary angiosarcoma is an uncommon malignant primary tumor of mesenchymal origin with very poor prognosis because it tends to infiltrate the heart and invades the surrounding structures. The diagnosis is made by cardiac imaging; transthoracic echocardiogram and transesophageal echocardiogram provide information about extension, implantation site, size and hemodynamic parameters related to the presence of the mass. Evaluation of the mass can include cardiac magnetic resonance and computerized cardiac tomography.

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References

Lam KY, Dickens P, Chan AC. Tumors of the heart: a 20-year experience with a review of 12,485 consecutive autopsies. Arch Pathol Lab Med 1993; 117: 1.027-1.031.

Engelen M, Bruch C, Hoffmeier A, et al. Primary left atrial angiosarcoma mimicking severe mitral valve stenosis. Heart 2005; 91: e27. DOI: https://doi.org/10.1136/hrt.2004.050872

Sinatra R, Brancaccio G, di Gioia CR, et al. Integrated approach for cardiac angiosarcoma. Int J Cardiol 2003; 88: 301-304. DOI: https://doi.org/10.1016/S0167-5273(02)00388-1

Meng Q, Lai H, Lima J, et al. Echocardiographic and pathologic characteristics of primary cardiac tumors: a study of 149 cases. Int J Cardiol 2002; 84: 69-75. DOI: https://doi.org/10.1016/S0167-5273(02)00136-5

Published

2018-08-31

How to Cite

1.
Rodríguez Israel M, Alvarado Sánchez E, Mena Sandí J, Moreno Medina E. Primary cardiac angiosarcoma. Rev Ecocardiogr Pract Otras Tec Imag Card (RETIC) [Internet]. 2018 Aug. 31 [cited 2024 Jul. 3];1(2):35-8. Available from: https://imagenretic.org/RevEcocarPract/article/view/161

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